Autoimmune ear disease: clinical and diagnostic relevance in Cogan’s sydrome

  • Luigi Maiolino | maiolino@policlinico.unict.it ENT Department, University of Catania, Italy.
  • Salvatore Cocuzza ENT Department, University of Catania, Italy.
  • Angelo Conti ENT Department, University of Catania, Italy.
  • Luisa Licciardello ENT Department, University of Catania, Italy.
  • Agostino Serra ENT Department, University of Catania, Italy.
  • Salvatore Gallina ENT Department, University of Palermo, Italy.

Abstract

The autoimmune inner ear disease is a clinical syndrome with uncertain pathogenesis that is often associated to rapidly progressive hearing loss that, especially at the early stages of disease, may be at monoaural localization, although more often it is at binaural localization. It usually occurs as a sudden deafness, or a rapidly progressive sensorineural hearing loss. In this study a particular form of autoimmune inner ear disease is described, Cogan’s syndrome. Cogan’s syndrome is a chronic inflammatory disorder that most commonly affects young adults. Clinical hallmarks are interstitial keratitis, vestibular and auditory dysfunction. Associations between Cogan’s syndrome and systemic vasculitis, as well as aortitis, also exist. We report a case of a young woman who presented audiological and systemic characteristics attributable to Cogan’s syndrome. In the description of the case we illustrate how the appearance and evolution of the disease presented.

Dimensions

Altmetric

PlumX Metrics

Downloads

Download data is not yet available.
Published
2017-03-30
Info
Issue
Section
Case Reports
Keywords:
Autoimmune ear disorder, Cogan’s syndrome, Hearing loss.
Statistics
  • Abstract views: 1293

  • PDF: 817
  • HTML: 417
How to Cite
Maiolino, L., Cocuzza, S., Conti, A., Licciardello, L., Serra, A., & Gallina, S. (2017). Autoimmune ear disease: clinical and diagnostic relevance in Cogan’s sydrome. Audiology Research, 7(1). https://doi.org/10.4081/audiores.2017.162